Langerhans Cell Histiocytosis: an orphan disease
نویسندگان
چکیده
منابع مشابه
Langerhans cell histiocytosis
Introduction: Langerhans cell histiocytosis (LCH), which was previously known as histiocytosis X, refers to a group of lesions that stimulate uncontrolled proliferation of cells. The purpose of this case was to report and describe a LCH case with mandibular bone involvement in a 2.5-year-old boy. Case reports: A 2.5 years old boy with LCH of mandibular jaw who has been treated by surgical inter...
متن کاملElements: in this month’s issue Langerhans Cell Histiocytosis: an orphan disease
There is no single agreed definition of a rare disease. The European Commission on Public Health defines rare diseases as those which are ‘life-threatening or chronically debilitating and which are of such low prevalence that special combined efforts are needed to address them’. The term ‘orphan’ has been used in association with rare diseases in order to emphasise their relative neglect in ter...
متن کاملCurrent Treatment Strategy in Langerhans Cell Histiocytosis
Langerhans cell histiocytosis (LCH) is a rare disorder described as three different entities including eosinophilic granulomaof bone, the Hand-Schuller-Christian syndrome, and Letterer-Siwe disease. LCH is currently classified into singlesystem LCH, and multisystem LCH. Patients with single system LCH have an excellent prognosis, and are mostlytreated with local therapy. Multisystem LCH is subd...
متن کاملHerpes Simplex Virus and Langerhans Cell Histiocytosis
Background and objective: Langerhans cell histiocytosis (LCH) is a rare histiocytic proliferative disorder of unknown etiology and mainly affects young children. The histological feature is granuloma-like proliferation of langerhans-type dendritic cells. Although the possible role of viruses such as Epstein-Barr virus (EBV, Human Herpes virus -4</...
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ژورنال
عنوان ژورنال: QJM
سال: 2011
ISSN: 1460-2725,1460-2393
DOI: 10.1093/qjmed/hcr006